英文名稱 |
Rabbit DES Polyclonal Antibody |
---|
應(yīng)用2 |
WB IHC |
克隆類型2 |
Polyclonal Antibody |
別名 |
CSM1;CSM2;LGMD2R
|
應(yīng)用 |
WB,IHC |
稀釋比例 |
WB1:500-1:2000 IHC1:50-1:100 |
交叉反應(yīng) |
Human Mouse Rat |
蛋白分子量 |
54kDa |
Gene ID |
1674 |
保存 |
Store at -20°C. Avoid freeze / thaw cycles.Stable for one year from the date of shipment. |
儲(chǔ)存液 |
PBS with 0.02% sodium azide, 50% glycerol, pH7.3. |
純化方法 |
Affinity purification |
亞型 |
IgG |
免疫原 |
Recombinant protein of human DES |
性狀 |
Lyophilized or Liquid |
Swiss Prot |
P17661 |
克隆類型 |
Polyclonal Antibody |
來源 |
Rabbit |
背景資料 |
This gene encodes a muscle-specific class III intermediate filament. Homopolymers of this protein form a stable intracytoplasmic filamentous network connecting myofibrils to each other and to the plasma membrane. Mutations in this gene are associated with desmin-related myopathy, a familial cardiac and skeletal myopathy (CSM), and with distal myopathies. |